Mutism after surgery in the posterior fossa
A hitherto unsolved postoperative phenomenon after surgical removal of midline tumors of the cerebellum in children is the so-called "cerebellar mutism" or "posterior fossa syndrome". Although the symptoms are usually temporary, the children often suffer from social and cognitive deficits in later life and the associated restrictions in quality of life. It is possible that injuries to midline structures, which can occur during neurosurgical procedures to remove such tumors, are involved. Which brain structures play a decisive role in this is not yet fully understood.
In experimental work, we have already shown that in adolescent rats, bilateral lesions of the fastigial nucleus, a very small brain region in the midline area of the cerebellum, lead to reduced social interaction and motor coordination during further development. In adulthood, additional cognitive deficits occur, the pattern of which shows parallels to the cognitive-affective cerebellar syndrome in humans. Electrophysiological measurements during various behavioral tasks show altered neuronal activity in frontal cortex areas. These findings suggest a modulatory function of the fastigial nucleus for higher cognitive processes.
Helgers SOA, Angelov S, Muschler MAN, Glahn A, Al-Afif S, Al Krinawe Y, Hermann EJ, Krauss JK, Frieling H, Schwabe K, Rhein M. Epigenetic Regulation of Neural Transmission after Cerebellar Fastigial Nucleus Lesions in Juvenile Rats. Cerebellum. 2021 Dec;20(6):922-930. DOI: 10.1007/s12311-021-01264-5
Helgers SOA, Al Krinawe Y, Alam M, Krauss JK, Schwabe K, Hermann EJ, Al-Afif S. Lesion of the Fastigial Nucleus in Juvenile Rats Deteriorates Rat Behavior in Adulthood, Accompanied by Altered Neuronal Activity in the Medial Prefrontal Cortex. Neuroscience. 2020 Aug 21;442:29-40. DOI: 10.1016/j.neuroscience.2020.06.035
Al-Afif S, Krauss JK, Helms F, Angelov S, John N, Schwabe K, Hermann EJ. Long-term impairment of social behavior, vocalizations and motor activity induced by bilateral lesions of the fastigial nucleus in juvenile rats. Brain Struct Funct. 2019 Jun;224(5):1739-1751. DOI: 10.1007/s00429-019-01871-3
Al-Afif S, Staden M, Krauss JK, Schwabe K, Hermann EJ. Splitting of the cerebellar vermis in juvenile rats--effects on social behavior, vocalization and motor activity. Behav Brain Res. 2013 Aug 1;250:293-8. DOI: 10.1016/j.bbr.2013.05.013
Hermann EJ, Rittierodt M, Krauss JK. Combined transventricular and supracerebellar infratentorial approach preserving the vermis in giant pediatric posterior fossa midline tumors. Neurosurgery. 2008 Jul;63(1 Suppl 1):ONS30-5; discussion ONS35-7. DOI: 10.1227/01.neu.0000335008.45499.22
Collaborations
Prof. Dr. Helge Frieling, Dr. Mathias Rhein (Clinical Department of Psychiatry, Social- and Psychological Therapy, MHH)
Sponsorship
Neurosurgical Research Foundation (DGNC)
German Childhood Cancer Foundation